This information is intended as a general introduction to this topic. As each person is affected differently by balance and dizziness problems, speak with your health care professional for individual advice.
What is hyperacusis?
Hyperacusis (hyper-ack-YOU-sis) a disorder in loudness perception. It is also called decreased sound tolerance or sound sensitivity. People with hyperacusis perceive certain everyday sounds as annoying, uncomfortable, painful, distressing and even terrifying. Hyperacusis can have a significant negative impact on activities of daily living. It can start gradually, or the onset can be sudden.
Trigger sounds are often high-pitched or start abruptly (impulse sounds) such as reversal beeps on trucks, pots and pans clattering, jingling coins, and dogs barking. Some people are bothered by continuous, low-pitched sounds such as computer fans, running water or refrigerator compressors. People with hyperacusis may have an increased awareness of sounds such as the ticking of a clock. Unexpected sounds, such as a balloon popping or screeching brakes, may bring about a strong startle response with hyperacusis.
As well as the more common loudness hyperacusis, a smaller number of people experience pain hyperacusis. With pain hyperacusis, some sounds bring on piercing head pain or migraine.
Some sounds make affected people anxious or fearful. This is called fear hyperacusis (phonophobia). Children with hyperacusis may struggle with sounds such as the washing machine or a hand dryer and refuse to go near the sound source.
Some trigger sounds, even soft ones such as other people chewing or a keyboard tapping, bring on an immediate strong reaction in people affected. This rare condition is referred to annoyance hyperacusis (misophonia). The reaction may range from annoyance to disgust, rage, panic or an immediate urge to flee. Annoyance hyperacusis sometimes has visual or olfactory (sense of smell) triggers.
Some sound-related symptoms may be confused with hyperacusis. These include:
- Tullio phenomenon – sound-induced dizziness. It is a rare symptom associated mainly with semicircular canal dehiscence syndrome (SCD).
- Recruitment – abnormal increase in the perception of loudness accompanied with hearing loss. With recruitment, loud noises seem uncomfortably loud; however, with hyperacusis, all sounds seem too loud.
Almost everyone finds some sounds annoying. For many, trigger sounds may be the screech of fingernails dragging down a blackboard or the repetitive drip of a leaky faucet. These are normal variations of sound intolerance, not hyperacusis.
Hyperacusis affects people of all ages. It is estimated that about 2 to 3% of people have some degree of hyperacusis. Only a small number of these are severely affected. About half of people with hyperacusis also have hearing loss.
More than 80% of patients with hyperacusis also have tinnitus (ringing in the ears). Hyperacusis can develop before, at the same time as, or after the onset of tinnitus. The frequent combination of hyperacusis and tinnitus suggests they may be caused by a similar mechanism.
What causes hyperacusis?
The mechanisms that provoke sound sensitivity are unclear. One theory is of abnormally increased sensitivity within the brain’s hearing system (increased auditory gain). If the brain were imagined as having a volume control dial, with hyperacusis the dial would be turned all the way up. Sounds that normally would be tolerated are perceived as too loud.
Other theories for why hyperacusis occurs include:
- malfunction of the ear’s protective hearing mechanisms
- damage to a portion of the auditory nerve
- a malfunction of the facial nerve
Decreased sound tolerance can be associated with a number of conditions, some of which are treatable, including:
- Ear-related (otologic): Ramsay Hunt Syndrome, Ménière’s disease, perilymph fistula, semicircular canal dehiscence (SCD), acoustic trauma (often caused by exposure to high-decibel noise), barotrauma (injuries caused by increased air or water pressure), noise-induced hearing loss, stapedectomy (surgery to remove a small bone from the middle ear to improve hearing), and tympanoplasty (surgery to repair a perforated eardrum)
- Neurologic: autism spectrum disorder (ASD), Bell’s palsy, carotid or middle cerebral aneurysm, migrainous cerebral infarction, head injury including concussion, Chiari malformation, sympathetic reflex dystrophy, multiple sclerosis, migraine, epilepsy, myasthenia gravis, cerebrospinal hypertonia, primary thalamo deficiency, attention-deficit disorder (ADD), anxiety and depression disorders, post-traumatic stress disorder (PTSD), and complication of spinal anaesthesia
- Endocrine: Addison’s disease, pan-hypopituitarism and hyperthyroidism
- Infection: neurosyphilis, Lyme disease and typhoid fever
- Medication: benzodiazepine and antidepressant withdrawal and acute phenytoin intoxication
- Vitamin and mineral deficiency: magnesium and pyridoxine (vitamin B6)
- Genetic or congenital: Williams syndrome, Idiopathic hypercalcemy (Fanconi and Williams-Beuren syndrome), Cri-du-Chat syndrome, Tay-Sachs disease, Cogan syndrome, GM1 gangliosidosis and spina bifida
- Other: temporomandibular joint (TMJ) disorder and fibromyalgia
The noise of an MRI scan may trigger or exacerbate hyperacusis. Scanning sequences for the internal auditory canal (IAC) are especially noisy. Hearing protection should be available and equipment can be set up to reduce noise exposure.
Diagnosis of hyperacusis
- pure-tone audiometry (a hearing test used to identify hearing thresholds)
- measurement of uncomfortable loudness levels
- a doctor or audiologist talking with the patient about how they perceive sound
Impact of living with hyperacusis
Some people feel they are sound sensitive but that it has minimal effect on activities of daily living. Those who are more severely impacted may become so fearful of sounds that they withdraw from normal activities in order to avoid sound.
- difficulty concentrating
- anxiety or even fear
- tension or even anger
Treatment and management
There is no quick cure to eliminate hyperacusis. However a combination of therapies can improve quality of life by reducing fear and anxiety, developing strategies to cope with uncomfortable sounds and even decreasing sound sensitivity.
Judicious use of hearing protection to muffle sounds in loud environments can help. Overuse of hearing protection in quiet environments, however, can trigger hyperacusis and likely makes existing hyperacusis worse.
Most researchers agree that people with tinnitus overuse hearing protection. Ask a hearing specialist for advice on when and how to best use hearing protection.
Treatment of associated medical conditions
Treatment options include:
Counselling, including cognitive behavioural therapy (CBT), to address emotions related to living with hyperacusis as well as any anxiety or depression that may contribute to sound intolerance. CBT can help patients change their pattern of thinking or behavior to lessen the impact of hyperacusis on their life. Note: it can be challenging to find a CBT practitioner who is knowledgeable about hearing disorders.
Education to understand that sound perceived as loud or uncomfortable is not necessarily causing permanent damage to hearing. If other people are not covering their ears or looking uncomfortable, then it is unlikely the sound is doing any damage.
Sound therapy to retrain the brain’s auditory processing centres to accept everyday sounds as normal again.
Sound generators worn in the ear may help some patients to gradually increase sound tolerance and reduce the contrast between bothersome noise and background noise.
Modified Tinnitus Retraining Therapy (TRT) has been shown to have an 85% success rate for people with misophonia.
Gradual exposure to increased sound in safe and predictable environments. This may mean slowly increasing sound levels when at home, or venturing out with ear protection that can be put on if needed.
Good quality electronic earmuffs may be suitable for hyperacusis and tinnitus patients exposed to intermittent noise. Their use can decrease overuse of hearing protection.
Patients who have sound-induced pain and temporary aural fullness (feeling of pressure or fullness in the ear) may be helped by a physiotherapist with special training in temporomandibular joint disorders (TMJ) and cervical (neck) treatment. This is particularly useful for those with a history of head or neck injury. Serious medical problems contributing to ear pain and aural fullness should be ruled out by medical assessment before seeing a physiotherapist for hyperacusis.
What to expect in the future
The speed and degree of recovery from hyperacusis varies from person to person. It may happen over weeks or months. Hyperacusis may improve by giving the ears time out or it may need specific treatment. It may fully resolve or there may be ongoing sound sensitivities necessitating changes in lifestyle or work.
The following can offer more help and support for affected individuals and their families.
Provides information on hyperacusis
A non-profit charity dedicated to the development of effective treatments for hyperacusis and to funding research that will eliminate the underlying mechanisms that cause hyperacusis.
An advocacy project, information site, and a resource to help bridge the gap between researchers, advocates, and sufferers (or concerned relatives).
Work Safe BC: Hearing Protection
Information on choosing and using hearing protection safely.
Allows those with misophonia to experience their favourite music and painlessly be exposed to tiny amounts of their triggers. iOS and Android versions.
Most of the following books are available for loan through public libraries in BC – if your local library does not own a copy of a title that interests you, ask for it to be sent from another library through inter-library loan.
Presents recent medical thinking and treatments, including sound therapy, and suggests effective self-help techniques based on cognitive behavioural therapy (CBT). Topics include: relaxation therapy, getting a good night’s sleep, avoiding relapse, and helping adults and children with these disorders.
Tinnitus Toolbox Hyperacusis Handbook covers currently available international science-based approaches including self-help, guided self-help, professional treatments, clinical trials, and experimental research. Written by a Vancouver audiologist who herself suffers from tinnitus.
Baguley D, McFerran, D, Hall, D. Tinnitus. The Lancet. 382:9904, p1600-1607. November 9, 2013. Available from: https://bit.ly/2JwgzR4
Colucci D. Effective management of pain hyperacusis. The Hearing Journal. 70:2, 242.44.45. February 2017. Available from: https://bit.ly/2Jv1S0s.
Pienkowski N. et al. A review of hyperacusis and future directions part II. Measurement, mechanisms, and treatment. American Journal of Audiology. 1 December 2014. Available from: https://bit.ly/2G0RJYw
Robb, MJA. A silver jubilee tribute to Pawel J. Jasterboff, PhD. Tinnitus Today. 40:3. p.14. Winter 2015. Available from: https://bit.ly/2LHDzPv
Tidball, G. The quick and dirty on hyperacusis. Canadian Audiologist2:2 2015. Available from: https://bit.ly/2S2veHh
Page updated August, 2019.
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